Author(s): YAO Juan, ZHAO Hongmei, YUAN Hongmei, DU Juan, LI Ping, TANG Mengmeng, WU Aiping
Pages: 285-286
Year: 2017 Issue:  3
Journal: Chinese Clinical Oncology
Keyword:  恶性蝾螈瘤; 恶性周围神经鞘膜瘤; Ⅰ型神经纤维瘤病; 临床病理特征;
Abstract: 恶性蝾螈瘤(malignant triton tumor,MTT)是伴有横纹肌肉瘤分化的恶性周围神经鞘膜瘤(malignant peripheral nerve sheath tumors,MPNSTs),是一种非常少见的恶性肿瘤,占MPNSTs的5%.本文报道1例伴发I型神经纤维瘤病(Neuraofibromatosis 1,NF-1)的发生于上肢的MTT,并结合相关文献,探讨MTT的临床病理特点及病理诊断与鉴别诊断.